Research Alerts

The latest publications on EDS from PubMed the most trusted source for medical research

Ehlers-Danlos syndrome

  • Diagnosing CAH-X syndrome by long-read sequencing and identifying a novel genotype
    Published: Apr 23, 2026
    Author: Zhen Li, Shiyi Xu, Qingxian Fu, Lingling Du, Qiuting Lin, Hongjie Lin, Huishu E, Hui Liu

    No abstract

  • Pregnancy in women with vascular Ehlers-Danlos syndrome: a case series from the registry of pregnancy and cardiac disease (ROPAC) III
    Published: Apr 20, 2026
    Author: P N J Peters, J A van der Zande, S K Prakash, J Harris, E Troost, D Tobler, B J Bouma, J W Roos-Hesselink, ROPAC investigators

    CONCLUSIONS: In women diagnosed with vEDS prior to pregnancy, the absence of life-threatening vascular events suggests pregnancy may be safer than previously reported. These findings support more individualized counseling and underscore the need for further prospective studies.

  • Intravenous 3-Dimensional Digital Subtraction Angiography: A Noninvasive, High-Quality Alternative to Cerebral Catheter Angiography
    Published: Apr 20, 2026
    Author: Kelsey M Bowman, Demi Dawkins, Sebastian Schaefer, James Scheuermann, Umid Sulaimanov, Azam S Ahmed, David Niemann, Mustafa K Baskaya, Beverly Aagaard-Kienitz

    CONCLUSION: With the newer, higher resolution, semirobotic biplane systems, IV 3D-DSA has become a tool in the angiography suite for rapid vascular assessment. It offers increased spatial resolution when compared with multidetector computed tomography, making it well suited to evaluate vasculature and endovascular devices, is noninvasive compared with catheter angiography, and can be used for intraoperative assessment of treatment.

  • Females with hypermobile Ehlers-Danlos syndrome self-report more sexual problems than chronic pain controls without hypermobility, males, or patients with hypermobile spectrum disorders
    Published: Apr 17, 2026
    Author: Cynthia E Neville, Frances C Wilson, DeLisa Fairweather, Melissa K Caywood, Katherine Gegoutchadze, Lincoln E Rozen, Nick A Farahani, Chrisandra L Shufelt, Dacre R T Knight, Shilpa N Gajarawala, Katelyn A Bruno

    CONCLUSIONS: This study is unique because we examine sex differences in sexual problems in patients with hEDS and HSD. Our findings indicate a higher percentage of sexual problems in females with hEDS than chronic pain controls without hypermobility, but this was not observed for females with HSD.

  • Durability of Mitral Valve Repair in Adult Connective Tissue Disease
    Published: Apr 17, 2026
    Author: Matthew Kazaleh, Catherine Wagner, Ricky Patil, Noor Pawar, China Green, Jessica Woodford, Robert B Hawkins, Matthew A Romano, Gorav Ailawadi, Steven F Bolling

    CONCLUSIONS: MVr can safely be performed in patients with CTD, with good short- and intermediate-term survival, as well as excellent durability. Mitral valve repair should be considered a standard of care in patients with connective tissue disease.

  • A safe seal: controlled flow arrest with dual balloon protection for embolisation of a large spontaneous splenic arteriovenous fistula-a case report
    Published: Apr 16, 2026
    Author: Preethi Vijayasekar, Tejesh Jagannathan, Karthik Kulanthaivelu, Sabarish Sekar, Ansan Joseph

    CONCLUSION: Dual-balloon-assisted coil and N-butyl cyanoacrylate (NBCA) embolisation enables precise, controlled flow arrest in high-flow SAA-SAVF, minimising non-target embolisation. This case highlights its value as a safe, spleen-preserving, and durable option-particularly relevant in patients with suspected connective-tissue disorders such as vEDS, where arterial fragility mandates meticulous endovascular technique.

  • Non-suicidal self-injury and suicide attempts among individuals seeking assessment for Ehlers-Danlos Syndromes
    Published: Apr 16, 2026
    Author: Callon M Williams, Rachel Siegal, Alisha Ratnasekera, Molly McCarthy, Michelle Flynn, Keisha Gobin, Laura McGillis, Nimish Mittal, Stephanie Buryk-Iggers, Tania Di Renna, Dmitry Rozenberg, Joel Katz, Hance Clarke, P Maxwell Slepian

    CONCLUSIONS: Joint hypermobility, BPD symptoms, and autonomic dysfunction may be important factors when examining rates of NSSI and suicide attempts among individuals being assessed for EDS/G-HSD. Given the high prevalence of NSSI and suicide attempts observed, future research should continue to investigate mechanisms and examine the effectiveness of psychological interventions for this population.

  • Tourniquet Use and Anesthesiology Considerations in Patients With Hypermobile Ehlers-Danlos Syndrome: Balancing Orthopedic Needs With Anesthetic Safety
    Published: Apr 14, 2026
    Author: Kaitlyn Unterman, Laith Fada, Kathleen A Clark, Julie Cherolis

    Hypermobile Ehlers-Danlos syndrome (hEDS) is a hereditary connective tissue disorder characterized by generalized joint hypermobility, soft tissue fragility, chronic pain, and autonomic dysfunction. Although major vascular complications are uncommon in hEDS, affected individuals frequently undergo orthopedic procedures, including ligament reconstructions, tendon repair, and joint stabilization, due to recurrent dislocations and musculoskeletal injury. Consequently, careful evaluation of...

  • The prevalence of dysautonomia in chronic musculoskeletal pain: a systematic review and meta-analysis
    Published: Apr 14, 2026
    Author: Norah A Almutairi, Darren C Greenwood, Manoj Sivan

    CONCLUSION: The high prevalence of dysautonomia in patients with chronic musculoskeletal painful conditions illustrates the association between dysautonomia and chronic pain, suggesting regular screening for dysautonomia is warranted for all patients with chronic musculoskeletal pain.

  • 2-Chloroprocaine vs. Lidocaine in a Patient With Hypermobile Ehlers-Danlos Syndrome and a History of Local Anesthetic Resistance: A Case Report
    Published: Apr 13, 2026
    Author: Jayanth Dasika, Zachary B Deutch, Amie L Hoefnagel

    Patients with hypermobile Ehlers-Danlos syndrome (hEDS) have a higher reported prevalence of local anesthetic (LA) resistance and obstetric complications than the general population. We describe a 33-year-old G2P0010 ASA III parturient with a history of hEDS and lidocaine resistance who presented for an anesthesia consultation in anticipation of possible neuraxial anesthesia. We surmised that performing a neuraxial procedure would require effective skin infiltration of the patient's lumbar area....

  • Spectrum of Respiratory Involvement in Ehlers-Danlos Syndrome: Insights From a Case Report
    Published: Apr 13, 2026
    Author: Arianna Andrade, Isabel Pava-Bernat, Luis Del Carpio, Galo Granados, Antía Ferreiro-Posse

    Vascular Ehlers-Danlos syndrome (vEDS) is a rare connective tissue disorder characterized by type III collagen deficiency and marked vascular fragility, which can lead to atypical thoracic manifestations and diagnostic uncertainty. We report a 30-year-old man who initially presented with an ischemic stroke due to arterial dissection and was later diagnosed with vEDS following identification of a pathogenic COL3A1 variant. During follow-up, he developed a large cavitary lung lesion initially...

  • Is treating both chronic pain and trauma-related symptoms at the same time effective? A systematic review and meta-analysis of psychological interventions
    Published: Apr 13, 2026
    Author: Brittany N Rosenbloom, Kathryn Curtis, Callon Williams, P Maxwell Slepian, Molly McCarthy, Michelle Flynn, Adriano Nella, Alice Kim, Rachel Siegal, Marina Englesakis, Karim S Ladha, Tania Di Renna, Rachael Bosma

    There is a large proportion of people living with chronic pain who also experience posttraumatic stress symptoms; however, there is no current standard treatment for addressing these mutually maintaining conditions. The aim of this systematic review and meta-analysis was to examine the efficacy of psychotherapeutic interventions for adults with chronic pain and trauma symptoms, where the effects of psychotherapy could be isolated. Systematic searches were conducted in 5 databases (MEDLINE,...

  • Comorbid Conditions of Ehlers-Danlos Syndromes and Vulvodynia: A Latent Class Analysis
    Published: Apr 12, 2026
    Author: Jennifer E Glayzer, Bethany C Bray, William H Kobak, Caleb M Trujillo, Crystal L Patil, Hongjin Li, Clair A Francomano, Judith M Schlaeger

    CONCLUSIONS: Phenotypes may constitute 1) different pathways for developing vulvodynia and/or 2) different subtypes of vulvodynia and/or EDS. We hypothesize that as a person accumulates comorbid conditions, their allostatic load increases, and once a personal allostatic load threshold is crossed, vulvodynia may develop.

  • Multimodal Wearable and Survey Data Reveal Distinct Physiologic Profiles in Hypermobile-Ehlers Danlos Syndrome for Screening Advancements
    Published: Apr 10, 2026
    Author: Damen Wilson, Maureen Shilling, Thomas Nowak, John M Wo, Clair A Francomano, Thomas Everett, Steven Steinhubl, Matthew Ward

    Hypermobile Ehlers-Danlos Syndrome (hEDS) is a genetic connective tissue disorder characterized by hypermobile joints, chronic pain, fatigue, brain fog, orthostatic intolerance, and GI symptoms and dysmotility. Its heterogeneous presentation contributes to poor quality of life, inappropriate interventions, and prolonged diagnostic delays, often up to 10 years. This study primarily aimed to determine if physiological signals captured by a medical-grade wrist wearable could characterize autonomic...

  • Bilateral optic neuritis and multiple nerve sheath tumors in a patient with genetically characterized Ehlers-Danlos syndrome: A rare co-occurrence
    Published: Apr 10, 2026
    Author: Byron R Larios A, Mildred Sabrina Mendoza Blandón, Silmalila Barahona Vargas, Christopher Kaleb Romero Ríos

    Classical‑like Ehlers-Danlos syndrome (clEDS) due to TNXB variants is a hereditary connective tissue disorder that shares clinical features with classic EDS but differs genetically from the COL5A1/COL5A2‑associated cEDS subtype. The coexistence of inflammatory optic neuropathy and multiple nerve sheath tumors in this context is rarely reported. We describe a 26-year-old woman with genetically characterized clEDS (TNXB variant) who presented with subacute bilateral visual loss. Orbital magnetic...

Stop searching!

Get information sent directly to your inbox!

Get involved in the movement to help find answers faster through community sharing. #Sharingiscaring

The information provided by EDS S.H.A.R.E. and EDS Joint Effort is not medical advice. It is intended for informational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the advice of your physician or other qualified health provider with any questions you may have regarding any medical condition. EDS Joint Effort, its producers, and its contents are not liable for any actions taken based on the information provided, and all users agree to hold harmless EDS Joint Effort and all products, producers from any claims arising from the use of the information provided. This information is not designed to replace a physician’s independent judgment about the appropriateness or risks for a given patient. Always consult your doctor about your medical conditions. EDS S.H.A.R.E. does not provide medical advice, diagnosis or treatment. Use of the site is conditional upon your acceptance of our Terms of Use and Privacy Policy as stated.